A steroid cell tumor outside the ovary is a rare cause of virilization.

OBJECTIVE: To report the case of a female who presented in childhood with symptoms and signs of hyperandrogenism secondary to an extraovarian steroid cell tumor.

DESIGN: Case report.

SETTING: Endocrine investigation unit of a university teaching hospital.

PATIENT(S): An 11-year-old female presented with symptoms and signs of hyperandrogenism.

INTERVENTION(S): Ultrasonography, MRI imaging, bilateral adrenal and ovarian venous sampling, laparoscopy, and laparotomy.

MAIN OUTCOME MEASURE(S): Ultrasonography, laboratory tests.

RESULT(S): Hyperandrogenism was due to an extraovarian steroid cell tumor located in the broad ligament. The tumor was successfully removed at laparotomy with biochemical and clinical resolution of the hyperandrogenism.

CONCLUSION(S): Extraovarian steroid cell tumor is a rare cause of hyperandrogenism.