Uterine didelphys with duplicated upper vagina and bilateral lower vaginal agenesis: a novel Müllerian anomaly with options for surgical management.

OBJECTIVE: To describe a novel Müllerian anomaly and management options.

DESIGN: Case series report.

SETTING: Metropolitan tertiary care children's hospital.

PATIENT(S): Three caucasian girls, aged 12, 13, and 15 years, with a novel congenital anomaly.

INTERVENTION(S): Interval staged vaginoplasties.

MAIN OUTCOME MEASURE(S): Functional vagina.

RESULT(S): Didelphys Müllerian development with vaginal duplication and agenesis of both lower vaginas with staged vaginoplasties resulting in normal functional vaginas.

CONCLUSION(S): Staged pull-through vaginoplasties led to functional outcome in this unusual anomaly.