Anatomical repair of double outlet right ventricle associated with complete atrioventricular septal defect and pulmonary stenosis: extending the indications for aortic translocation.

The combination of double outlet right ventricle (DORV) and complete atrioventricular septal defect (CAVSD) remains a surgical challenge for anatomical repair. Inasmuch as the ventricular septal defect is noncommitted in this combination, the major concern regarding anatomical repair is the reconstruction of the unobstructed left ventricular outflow tract without compromising right ventricular volume and the right ventricular outflow tract. We report on a patient who underwent an anatomical repair using aortic root translocation for DORV with CAVSD and pulmonary stenosis (PS).