Pigmented neuroectodermal tumor of infancy. An example of rarely expressed malignant behavior.

A 4-month-old patient presented with a melanotic neuroectodermal tumor. The tumor continued to progress and recur following each surgical intervention and the patient died at the age of 38 months, 36 months following discovery of the tumor. This article describes the clinical and pathologic features of the disease. At autopsy, the tumor resembled that of a neuroblastoma.